LUONI, MIRKO
LUONI, MIRKO
Istituto di Neuroscienze - IN - Sede Secondaria Milano
Microglia-specific IL-10 gene delivery inhibits neuroinflammation and neurodegeneration in a mouse model of Parkinson’s disease
2024 Bido, Simone; Nannoni, Melania; Muggeo, Sharon; Gambarè, Diana; Ruffini, Giorgia; Bellini, Edoardo; Passeri, Laura; Iaia, Silvia; Luoni, Mirko; Provinciali, Martino; Giannelli, Serena Gea; Giannese, Francesca; Lazarevic, Dejan; Gregori, Silvia; Broccoli, Vania
New AAV9 engineered variants with enhanced neurotropism and reduced liver off-targeting in mice and marmosets
2024 Giannelli, Serena Gea; Luoni, Mirko; Iannielli, Angelo; Middeldorp, Jinte; Philippens, Ingrid; Bido, Simone; Körbelin, Jakob; Broccoli, Vania
Genome-wide screening in pluripotent cells identifies Mtf1 as a suppressor of mutant huntingtin toxicity
2023 Ferlazzo, Giorgia Maria; Gambetta, Anna Maria; Amato, Sonia; Cannizzaro, Noemi; Angiolillo, Silvia; Arboit, Mattia; Diamante, Linda; Carbognin, Elena; Romani, Patrizia; La Torre, Federico; Galimberti, Elena; Pflug, Florian; Luoni, Mirko; Giannelli, Serena; Pepe, Giuseppe; Capocci, Luca; Di Pardo, Alba; Vanzani, Paola; Zennaro, Lucio; Broccoli, Vania; Leeb, Martin; Moro, Enrico; Maglione, Vittorio; Martello, Graziano
MCT1-dependent energetic failure and neuroinflammation underlie optic nerve degeneration in Wolfram syndrome mice
2023 Rossi, Greta; Ordazzo, Gabriele; Vanni, Niccolò N; Castoldi, Valerio; Iannielli, Angelo; Di Silvestre, Dario; Bellini, Edoardo; Bernardo, Letizia; Giannelli, Serena G; Luoni, Mirko; Muggeo, Sharon; Leocani, Letizia; Mauri, Pierluigi; Broccoli, Vania
Modeling native and seeded Synuclein aggregation and related cellular dysfunctions in dopaminergic neurons derived by a new set of isogenic iPSC lines with SNCA multiplications
2022 Iannielli, Angelo; Luoni, Mirko; Giannelli, Serena Gea; Ferese, Rosangela; Ordazzo, Gabriele; Fossati, Matteo; Raimondi, Andrea; Opazo, Felipe; Corti, Olga; Prehn, Jochen H.M.; Gambardella, Stefano; Melki, Ronald; Broccoli, Vania
SETBP1 accumulation induces P53 inhibition and genotoxic stress in neural progenitors underlying neurodegeneration in Schinzel-Giedion syndrome
2021 Banfi, F; Rubio, A; Zaghi, M; Massimino, L; Fagnocchi, G; Bellini, E; Luoni, M; Cancellieri, C; Bagliani, A; Di Resta, C; Maffezzini, C; Ianielli, A; Ferrari, M; Piazza, R; Mologni, L; Broccoli, V; Sessa, A
Frataxin gene editing rescues Friedreich's ataxia pathology in dorsal root ganglia organoid-derived sensory neurons
2020 Mazzara, Pg; Muggeo, S; Luoni, M; Massimino, L; Zaghi, M; Valverde, Ptt; Brusco, S; Marzi, Mj; Palma, C; Colasante, G; Iannielli, A; Paulis, M; Cordiglieri, C; Giannelli, Sg; Podini, P; Gellera, C; Taroni, F; Nicassio, F; Rasponi, M; Broccoli, V
Whole brain delivery of an instability-prone Mecp2 transgene improves behavioral and molecular pathological defects in mouse models of Rett syndrome
2020 Luoni, M; Giannelli, S; Indrigo, Mt; Niro, A; Massimino, L; Iannielli, A; Passeri, L; Russo, F; Morabito, G; Calamita, P; Gregori, S; Deverman, B; Broccoli, V
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| Microglia-specific IL-10 gene delivery inhibits neuroinflammation and neurodegeneration in a mouse model of Parkinson’s disease | 1-gen-2024 | Bido, Simone; Nannoni, Melania; Muggeo, Sharon; Gambarè, Diana; Ruffini, Giorgia; Bellini, Edoardo; Passeri, Laura; Iaia, Silvia; Luoni, Mirko; Provinciali, Martino; Giannelli, Serena Gea; Giannese, Francesca; Lazarevic, Dejan; Gregori, Silvia; Broccoli, Vania | |
| New AAV9 engineered variants with enhanced neurotropism and reduced liver off-targeting in mice and marmosets | 1-gen-2024 | Giannelli, Serena Gea; Luoni, Mirko; Iannielli, Angelo; Middeldorp, Jinte; Philippens, Ingrid; Bido, Simone; Körbelin, Jakob; Broccoli, Vania | |
| Genome-wide screening in pluripotent cells identifies Mtf1 as a suppressor of mutant huntingtin toxicity | 1-gen-2023 | Ferlazzo, Giorgia Maria; Gambetta, Anna Maria; Amato, Sonia; Cannizzaro, Noemi; Angiolillo, Silvia; Arboit, Mattia; Diamante, Linda; Carbognin, Elena; Romani, Patrizia; La Torre, Federico; Galimberti, Elena; Pflug, Florian; Luoni, Mirko; Giannelli, Serena; Pepe, Giuseppe; Capocci, Luca; Di Pardo, Alba; Vanzani, Paola; Zennaro, Lucio; Broccoli, Vania; Leeb, Martin; Moro, Enrico; Maglione, Vittorio; Martello, Graziano | |
| MCT1-dependent energetic failure and neuroinflammation underlie optic nerve degeneration in Wolfram syndrome mice | 1-gen-2023 | Rossi, Greta; Ordazzo, Gabriele; Vanni, Niccolò N; Castoldi, Valerio; Iannielli, Angelo; Di Silvestre, Dario; Bellini, Edoardo; Bernardo, Letizia; Giannelli, Serena G; Luoni, Mirko; Muggeo, Sharon; Leocani, Letizia; Mauri, Pierluigi; Broccoli, Vania | |
| Modeling native and seeded Synuclein aggregation and related cellular dysfunctions in dopaminergic neurons derived by a new set of isogenic iPSC lines with SNCA multiplications | 1-gen-2022 | Iannielli, Angelo; Luoni, Mirko; Giannelli, Serena Gea; Ferese, Rosangela; Ordazzo, Gabriele; Fossati, Matteo; Raimondi, Andrea; Opazo, Felipe; Corti, Olga; Prehn, Jochen H.M.; Gambardella, Stefano; Melki, Ronald; Broccoli, Vania | |
| SETBP1 accumulation induces P53 inhibition and genotoxic stress in neural progenitors underlying neurodegeneration in Schinzel-Giedion syndrome | 1-gen-2021 | Banfi, F; Rubio, A; Zaghi, M; Massimino, L; Fagnocchi, G; Bellini, E; Luoni, M; Cancellieri, C; Bagliani, A; Di Resta, C; Maffezzini, C; Ianielli, A; Ferrari, M; Piazza, R; Mologni, L; Broccoli, V; Sessa, A | |
| Frataxin gene editing rescues Friedreich's ataxia pathology in dorsal root ganglia organoid-derived sensory neurons | 1-gen-2020 | Mazzara, Pg; Muggeo, S; Luoni, M; Massimino, L; Zaghi, M; Valverde, Ptt; Brusco, S; Marzi, Mj; Palma, C; Colasante, G; Iannielli, A; Paulis, M; Cordiglieri, C; Giannelli, Sg; Podini, P; Gellera, C; Taroni, F; Nicassio, F; Rasponi, M; Broccoli, V | |
| Whole brain delivery of an instability-prone Mecp2 transgene improves behavioral and molecular pathological defects in mouse models of Rett syndrome | 1-gen-2020 | Luoni, M; Giannelli, S; Indrigo, Mt; Niro, A; Massimino, L; Iannielli, A; Passeri, L; Russo, F; Morabito, G; Calamita, P; Gregori, S; Deverman, B; Broccoli, V |