IANNIELLI, ANGELO

IANNIELLI, ANGELO  

Istituto di Neuroscienze - IN -  

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Risultati 1 - 6 di 6 (tempo di esecuzione: 0.01 secondi).
Titolo Data di pubblicazione Autore(i) File
Exploiting hiPSCs in Leber's Hereditary Optic Neuropathy (LHON): Present Achievements and Future Perspectives 1-gen-2021 Peron, C; Maresca, A; Cavaliere, A; Iannielli, A; Broccoli, V; Carelli, V; Di Meo, I; Tiranti, V
Generation of two human iPSC lines, FINCBi002-A and FINCBi003-A, carrying heteroplasmic macrodeletion of mitochondrial DNA causing Pearson's syndrome 1-gen-2021 Peron C.; Mauceri R.; Iannielli A.; Cavaliere A.; Legati A.; Rizzo A.; Sciacca F.L.; Broccoli V.; Tiranti V.
The relevance of mitochondrial DNA variants fluctuation during reprogramming and neuronal differentiation of human iPSCs 1-gen-2021 Palombo, F; Peron, C; Caporali, L; Iannielli, A; Maresca, A; Di Meo, I; Fiorini, C; Segnali, A; Sciacca, Fl; Rizzo, A; Levi, S; Suomalainen, A; Prigione, A; Broccoli, V; Carelli, V; Tiranti, V
Frataxin gene editing rescues Friedreich's ataxia pathology in dorsal root ganglia organoid-derived sensory neurons 1-gen-2020 Mazzara, Pg; Muggeo, S; Luoni, M; Massimino, L; Zaghi, M; Valverde, Ptt; Brusco, S; Marzi, Mj; Palma, C; Colasante, G; Iannielli, A; Paulis, M; Cordiglieri, C; Giannelli, Sg; Podini, P; Gellera, C; Taroni, F; Nicassio, F; Rasponi, M; Broccoli, V
Generation of a human iPSC line, FINCBi001-A, carrying a homoplasmic m.G3460A mutation in MT-ND1 associated with Leber's Hereditary optic Neuropathy (LHON) 1-gen-2020 Peron C.; Mauceri R.; Cabassi T.; Segnali A.; Maresca A.; Iannielli A.; Rizzo A.; Sciacca F.L.; Broccoli V.; Carelli V.; Tiranti V.
Whole brain delivery of an instability-prone Mecp2 transgene improves behavioral and molecular pathological defects in mouse models of Rett syndrome 1-gen-2020 Luoni, M; Giannelli, S; Indrigo, Mt; Niro, A; Massimino, L; Iannielli, A; Passeri, L; Russo, F; Morabito, G; Calamita, P; Gregori, S; Deverman, B; Broccoli, V