STRINA, DARIO

STRINA, DARIO  

Istituto di Ricerca Genetica e Biomedica - IRGB - Sede Secondaria Milano  

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Titolo Data di pubblicazione Autore(i) File
Deletion of Dipeptidyl peptidase 3 in mice unleashes protective antibacterial immunity against Klebsiella pneumoniae 1-gen-2024 Facoetti, Amanda; Lambroia, Luca; Fontana, Elena; Strina, Dario; Lucia Schiavone, Maria; Nicchiotti, Federico; Menale, Ciro; Garlanda, Cecilia; Sobacchi, Cristina; Marrella, Veronica; Cassani, Barbara
Exonic knockout and knockin gene editing in hematopoietic stem and progenitor cells rescues RAG1 immunodeficiency 1-gen-2024 Castiello, Maria Carmina; Brandas, Chiara; Ferrari, Samuele; Porcellini, Simona; Sacchetti, Nicolò; Canarutto, Daniele; Draghici, Elena; Merelli, Ivan; Barcella, Matteo; Pelosi, Gabriele; Vavassori, Valentina; Varesi, Angelica; Jacob, Aurelien; Scala, Serena; Basso Ricci, Luca; Paulis, Marianna; Strina, Dario; Di Verniere, Martina; Sergi Sergi, Lucia; Serafini, Marta; Holland, Steven M.; Bergerson, Jenna R. E.; De Ravin, Suk See; Malech, Harry L.; Pala, Francesca; Bosticardo, Marita; Brombin, Chiara; Cugnata, Federica; Calzoni, Enrica; Crooks, Gay M.; Notarangelo, Luigi D.; Genovese, Pietro; Naldini, Luigi; Villa, Anna
Interleukin-1β Polymorphisms Are Genetic Markers of Susceptibility to Periprosthetic Joint Infection in Total Hip and Knee Arthroplasty 1-gen-2024 Granata, V.; Strina, D.; Possetti, V.; Leone, R.; Valentino, S.; Chiappetta, K.; Loppini, M.; Mantovani, A.; Bottazzi, B.; Asselta, R.; Sobacchi, C.; Inforzato, A.
Genetic Deficiency of the Long Pentraxin 3 Affects Osteogenesis and Osteoclastogenesis in Homeostatic and Inflammatory Conditions 1-gen-2023 Granata, V.; Strina, D.; Schiavone, M. L.; Bottazzi, B.; Mantovani, A.; Inforzato, A.; Sobacchi, C.
A novel intronic variant in PIGB in Acrofrontofacionasal dysostosis type 1 patients expands the spectrum of phenotypes associated with GPI biosynthesis defects 1-gen-2021 Palagano E.; Gordon C.T.; Uva P.; Strina D.; Dimartino C.; Villa A.; Amiel J.; GuionAlmeida M.L.; VendraminiPittoli S.; KokitsuNakata N.M.; ZechiCeide R.M.; Sobacchi C.
Generation of an immunodeficient mouse model of tcirg1-deficient autosomal recessive osteopetrosis 1-gen-2020 Palagano, E; Muggeo, S; Crisafulli, L; Tourkova, Il; Strina, D; Mantero, S; Fontana, E; Locatelli, Sl; Monari, M; Morenghi, E; Carlostella, C; Barnett, Jb; Blair, Hc; Vezzoni, P; Villa, A; Sobacchi, C; Ficara, F
Absence of Dipeptidyl Peptidase 3 Increases Oxidative Stress and Causes Bone Loss 1-gen-2019 Menale, C; Robinson, Lj; Palagano, E; Rigoni, R; Erreni, M; Almarza, Aj; Strina, D; Mantero, S; Lizier, M; Forlino, A; Besio, R; Monari, M; Vezzoni, P; Cassani, B; Blair, Hc; Villa, A; Sobacchi, C
Chromosome Transplantation: Correction of the Chronic Granulomatous Disease Defect in Mouse Induced Pluripotent Stem Cells 1-gen-2019 Castelli, A; Susani, L; Menale, C; Muggeo, S; Caldana, E; Strina, D; Cassani, B; Recordati, C; Scanziani, E; Ficara, F; Villa, A; Vezzoni, P; Paulis, M
RANK-dependent autosomal recessive osteopetrosis: characterisation of 5 new cases with novel mutations. 1-gen-2012 Pangrazio A; Cassani B; Guerrini MM; Crockett JC; Marrella V; Zammataro L; Strina D; Schulz A; Schlack C; Kornak U; Mellis DJ; Duthie A; Helfrich MH; Durandy A; Moshous D; Vellodi A; Chiesa R; Veys P; Lo Iacono N; Vezzoni P; Fischer A; Villa A; Sobacchi C.
Homeostatic expansion of autoreactive immunoglobulin-secreting cells in the Rag2 mouse model of Omenn syndrome. 1-gen-2010 Cassani, B; Poliani, Pl; Marrella, V; Schena, F; Sauer, Av; Ravanini, M; Strina, D; Busse, Ce; Regenass, S; Wardemann, H; Martini, A; Facchetti, F; van der Burg, M; Rolink, Ag; Vezzoni, P; Grassi, F; Traggiai, E; Villa, A
Characterization of nine novel mutations in the CD40 ligand gene in patients with X-linked hyper IgM syndrome of various ancestry. 1-gen-1995 Macchi, Paolo; Villa, Anna; Strina, Dario; Grazia Sacco, Maria; Morali, Federica; Brugnoni, Duilio; Giliani, Silvia; Mantuano, Elide; Fasth, Anders; Andersson, Bengt; M Zegers, Ben J; Cavagni, Giovanni; Reznick, Igor; Levy, Jacov; Zanbar, Israel; Porat, Yael; Airo, Paolo; Plebani, Alessandro; Vezzoni, Paolo; D Notarangelo, Luigi
X-linked thrombocytopenia and Wiskott-Aldrich syndrome are allelic diseases with mutations in the WASP gene 1-gen-1995 Villa, Anna; Notarangelo, Luigi; Macchi, Paolo; Mantuano, Elide; Cavagni, Giovanni; Brugnoni, Duilio; Strina, Dario; Cristina Patrosso, M; Ramenghi, Ugo; Grazia Sacco, Maria; Ugazio, Alberto; Vezzoni, Paolo