VEZZONI, PAOLO MARIA

VEZZONI, PAOLO MARIA  

Istituto di Ricerca Genetica e Biomedica - IRGB  

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Risultati 1 - 20 di 99 (tempo di esecuzione: 0.025 secondi).
Titolo Data di pubblicazione Autore(i) File
PBX1-directed stem cell transcriptional program drives tumor progression in myeloproliferative neoplasm 1-gen-2021 Muggeo, Sharon; Crisafulli, Laura; Uva, Paolo; Fontana, Elena; Ubezio, Marta; Morenghi, Emanuela; Colombo, Federico Simone; Rigoni, Rosita; Peano, Clelia; Vezzoni, Paolo; Della Porta, Matteo Giovanni; Villa, Anna; Ficara, Francesca
Chromosome Transplantation: A Possible Approach to Treat Human X-linked Disorders 1-gen-2020 Paulis, M; Susani, L; Castelli, A; Suzuki, T; Hara, T; Straniero, L; Duga, S; Strina, D; Mantero, S; Caldana, E; Sergi, Ls; Villa, A; Vezzoni, P
Generation of 3 clones of induced pluripotent stem cells (iPSCs) from a patient affected by Autosomal Recessive Osteopetrosis due to mutations in TCIRG1 gene. 1-gen-2020 Lanzi, G; Ferraro, Rm; Masneri, S; Piovani, G; Barisani, C; Sobacchi, C; Villa, A; Vezzoni, P; Giliani, S
Generation of an immunodeficient mouse model of tcirg1-deficient autosomal recessive osteopetrosis 1-gen-2020 Palagano E.; Muggeo S.; Crisafulli L.; Tourkova I.L.; Strina D.; Mantero S.; Fontana E.; Locatelli S.L.; Monari M.; Morenghi E.; CarloStella C.; Barnett J.B.; Blair H.C.; Vezzoni P.; Villa A.; Sobacchi C.; Ficara F.
Chromosome Transplantation: Correction of the Chronic Granulomatous Disease Defect in Mouse Induced Pluripotent Stem Cells 1-gen-2019 Castelli A.; Susani L.; Menale C.; Muggeo S.; Caldana E.; Strina D.; Cassani B.; Recordati C.; Scanziani E.; Ficara F.; Villa A.; Vezzoni P.; Paulis M.
Generation of 3 clones of induced pluripotent stem cells (iPSCs) from a patient affected by Autosomal Recessive Osteopetrosis due to mutations in TCIRG1 gene. 1-gen-2019 Lanzi, G; Ferraro, Rm; Masneri, S; Piovani, G; Barisani, C; Sobacchi, C; Villa, A; Vezzoni, P; Giliani, S
Motor neuron degeneration, severe myopathy and TDP-43 increase in a transgenic pig model of SOD1-linked familiar ALS 1-gen-2019 Crociara P.; Chieppa M.N.; Vallino Costassa E.; Berrone E.; Gallo M.; Lo Faro M.; Pintore M.D.; Iulini B.; D'Angelo A.; Perona G.; Botter A.; Formicola D.; Rainoldi A.; Paulis M.; Vezzoni P.; Meli F.; Peverali F.A.; Bendotti C.; Trolese M.C.; Pasetto L.; Bonetto V.; Lazzari G.; Duchi R.; Perota A.; Lagutina I.; Quadalti C.; Gennero M.S.; Dezzutto D.; Desiato R.; Boido M.; Ghibaudi M.; Valentini M.C.; Caramelli M.; Galli C.; Casalone C.; Corona C.
The K219T-Lamin mutation induces conduction defects through epigenetic inhibition of SCN5A in human cardiac laminopathy 1-gen-2019 Salvarani, N; Crasto, S; Miragoli, M; Bertero, A; Paulis, M; Kunderfranco, P; Serio, S; Forni, A; Lucarelli, C; Dal Ferro, M; Larcher, V; Sinagra, G; Vezzoni, P; Murry, Ce; Faggian, G; Condorelli, G; Di Pasquale, E
Cell fusion in the liver, revisited 1-gen-2018 Lizier, Michela; Castelli, Alessandra; Montagna, Cristina; Lucchini, Franco; Vezzoni, Paolo; Faggioli, Francesca
Motor neuron degeneration, severe myopathy and TDP-43 increase in a transgenic pig model of SOD1-linked familiar ALS. 1-gen-2018 Crociara, P; Chieppa, Mn; Vallino Costassa, E; Berrone, E; Gallo, M; Lo Faro, M; Pintore, Md; Iulini, B; D'Angelo, A; Perona, G; Botter, A; Formicola, D; Rainoldi, A; Paulis, M; Vezzoni, P; Meli, F; Peverali, Fa; Bendotti, C; Trolese, Mc; Pasetto, L; Bonetto, V; Lazzari, G; Duchi, R; Perota, A; Lagutina, I; Quadalti, C; Gennero, Ms; Dezzutto, D; Desiato, R; Boido, M; Ghibaudi, M; Valentini, Mc; Caramelli, M; Galli, C; Casalone, C; Corona, C
Mutations in the Neuroblastoma Amplified Sequence gene in a family affected by Acrofrontofacionasal Dysostosis type 1 1-gen-2018 Palagano, E; Zuccarini, G; Prontera, P; Borgatti, R; Stangoni, G; Elisei, S; Mantero, S; Menale, C; Forlino, A; Uva, P; Oppo, M; Vezzoni, P; Villa, A; Merlo, Gr; Sobacchi, C
B lymphocytes limit senescence-driven fibrosis resolution and favor hepatocarcinogenesis in mouse liver injury. 1-gen-2017 Faggioli, Francesca; Palagano, Eleonora; Di Tommaso, Luca; Donadon, Matteo; Marrella, Veronica; Recordati, Camilla; Mantero, Stefano; Villa, Anna; Vezzoni, Paolo; Cassani, Barbara
Fusion between cancer cells and macrophages occurs in a murine model of spontaneous neu+ breast cancer without increasing its metastatic potential 1-gen-2016 Lizier, M; Anselmo, A; Mantero, S; Ficara, F; Paulis, M; Vezzoni, P; Lucchini, F; Pacchiana, G
Intestinal microbiota sustains inflammation and autoimmunity induced by hypomorphic RAG defects 1-gen-2016 Rigoni, R; Fontana, E; Guglielmetti, S; Fosso, B; D'Erchia, Am; Maina, V; Taverniti, V; Castiello, Mc; Mantero, S; Pacchiana, G; Musio, S; Pedotti, R; Selmi, C; Rodrigo Mora, J; Pesole, G; Vezzoni, P; Poliani, Pl; Grassi, F; Villa, A; Cassani, B
Synonymous Mutations Add a Layer of Complexity in the Diagnosis of Human Osteopetrosis. 1-gen-2016 Palagano, E; Susani, L; Menale, C; Ramenghi, U; Berger, M; Uva, P; Oppo, M; Vezzoni, P; Villa, A; Sobacchi, C
A pre-screening FISH-based method to detect CRISPR/Cas9 off-targets in mouse embryonic stem cells 1-gen-2015 Paulis, M; Castelli, A; Lizier, M; Susani, L; Lucchini, F; Villa, A; Vezzoni, P
Chromosome transplantation as a novel approach for correcting complex genomic disorders 1-gen-2015 Paulis M.; Castelli A.; Susani L.; Lizier M.; Lagutina I.; Focarelli M.L.; Recordati C.; Uva P.; Faggioli F.; Neri T.; Scanziani E.; Galli C.; Lucchini F.; Villa A.; Vezzoni P.
Dendritic cells cause bone lesions in a new mouse model of histiocytosis 1-gen-2015 Grosjean F.; Nasi S.; Schneider P.; Chobaz V.; Liu A.; Mordasini V.; Moullec K.; Vezzoni P.; Lavanchy C.; Busso N.; AchaOrbea H.; Ehirchiou D.
IL-10 Critically Modulates B Cell Responsiveness in Rankl(-/-) Mice 1-gen-2015 Marrella, VERONICA AGATA; Lo Iacono, Nadia; Fontana, Elena; Sobacchi, Cristina; Sic, Heiko; Schena, Francesca; Sereni, Lucia; Castiello Maria, Carmina; Poliani Pietro, Luigi; Vezzoni, PAOLO MARIA; Cassani, Barbara; Traggiai, Elisabetta; Villa, Anna
Targeted gene correction in osteopetrotic-induced pluripotent stem cells for the generation of functional osteoclasts 1-gen-2015 Neri T.; Muggeo S.; Paulis M.; Caldana M.E.; Crisafulli L.; Strina D.; Focarelli M.L.; Faggioli F.; Recordati C.; Scaramuzza S.; Scanziani E.; Mantero S.; Buracchi C.; Sobacchi C.; Lombardo A.; Naldini L.; Vezzoni P.; Villa A.; Ficara F.