BRANCACCIO, ANDREA

BRANCACCIO, ANDREA  

Istituto di Scienze e Tecnologie Chimiche "Giulio Natta" - SCITEC - Sede Secondaria Roma  

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Analysis of the GFP-labelled β-dystroglycan interactome in HEK-293 transfected cells reveals novel intracellular networks 1-gen-2024 Sciandra, Francesca; Desiderio, Claudia; Vincenzoni, Federica; Viscuso, Simona; Bozzi, Manuela; Hübner, Wolfgang; Jimenez-Gutierrez, Guadalupe Elizabeth; Cisneros, Bulmaro; Brancaccio, Andrea
The consequence of ATP synthase dimer angle on mitochondrial morphology studied by cryo-electron tomography 1-gen-2024 Buzzard, E.; Mclaren, M.; Bragoszewski, P.; Brancaccio, A.; Ford, H. C.; Daum, B.; Kuwabara, P.; Collinson, I.; Gold, V. A. M.
The missense mutation C667F in murine β-dystroglycan causes embryonic lethality, myopathy and blood-brain barrier destabilization 1-gen-2024 Lois Tan, Rui; Sciandra, Francesca; Hübner, Wolfgang; Bozzi, Manuela; Reimann, Jens; Schoch, Susanne; Brancaccio, Andrea; Blaess, Sandra
The α-dystroglycan N-terminus is a broad-spectrum antiviral agent against SARS-CoV-2 and enveloped viruses 1-gen-2024 Bigotti, M. G.; Klein, K.; Gan, E. S.; Anastasina, M.; Andersson, S.; Vapalahti, O.; Katajisto, P.; Erdmann, M.; Davidson, A. D.; Butcher, S. J.; Collinson, I.; Ooi, E. E.; Balistreri, G.; Brancaccio, A.; Yamauchi, Y.
Verbascoside Elicits Its Beneficial Effects by Enhancing Mitochondrial Spare Respiratory Capacity and the Nrf2/HO-1 Mediated Antioxidant System in a Murine Skeletal Muscle Cell Line 1-gen-2023 Sciandra, F.; Bottoni, P.; De Leo, M.; Braca, A.; Brancaccio, A.; Bozzi, M.
Determination of Agrin and Related Proteins Levels as a Function of Age in Human Hearts 1-gen-2022 Skeffington, Kl; Jones, Fp; Suleiman, Ms; Caputo, M; Brancaccio, A; Bigotti, Mg
High degree of conservation of the enzymes synthesizing the laminin-binding glycoepitope of alpha-dystroglycan 1-gen-2021 Bigotti, Mg; Brancaccio, A
Agrin-Mediated Cardiac Regeneration: Some Open Questions 1-gen-2020 Bigotti, Mg; Skeffington, Kl; Jones, Fp; Caputo, M; Brancaccio, A
Identification and Modeling of a GT-A Fold in the ?-Dystroglycan Glycosylating Enzyme LARGE1 1-gen-2020 Righino, B; Bozzi, M; Bozzi, M; Pirolli, D; Sciandra, F; Bigotti, Mg; Bigotti, Mg; Brancaccio, A; Brancaccio, A; DE ROSA, MARIA CRISTINA
Identification and Modeling of a GT-A Fold in the α-Dystroglycan Glycosylating Enzyme LARGE1 1-gen-2020 Righino, Benedetta; Bozzi, Manuela; Pirolli, Davide; Sciandra, Francesca; Bigotti, Maria Giulia; Brancaccio, Andrea; De Rosa, Maria Cristina
Loss of dystroglycan drives cellular senescence via defective mitosis-mediated genomic instability 1-gen-2020 Jimenez-Gutierrez, G. E.; Mondragon-Gonzalez, R.; Soto-Ponce, L. A.; Gomez-Monsivais, W. L.; Garcia-Aguirre, I.; Pacheco-Rivera, R. A.; Suarez-Sanchez, R.; Brancaccio, A.; Magana, J. J.; Perlingeiro, R. C. R.; Cisneros, B.
The molecular basis and biologic significance of the beta-dystroglycan-emerin interaction 1-gen-2020 Gomezmonsivais, Wl; Monterrubioledezma, F; Huertacantillo, J; Mondragongonzalez, R; Alamilloiniesta, A; Garciaaguirre, I; Azuaramedina, Pm; Arguellogarcia, R; Riveramonroy, Je; Holaska, Jm; Hernandezmendez, Jme; Garrido, E; Magana, Jj; Winder, Sj; Brancaccio, A; Martinezvieyra, I; Navarrogarcia, F; Cisneros, B
A molecular overview of the primary dystroglycanopathies 1-gen-2019 Brancaccio, Andrea; Brancaccio, Andrea
A primary dystroglycanopathy causing muscle-eye-brain disease with multicystic leukodystrophy: from cellular and biochemical analysis to a mouse model 1-gen-2019 Francesca Sciandra; Manuela Bozzi; Maria Giulia Bigotti; Alberto Cassetta; Sonia Covaceuszach; Wolfgang Hübner; Thomas Huser; CarolAnn Eberle; Natalia Niemir; Sandra Blaess; Andrea Brancaccio
Analysis of alpha-Dystroglycan/LG Domain Binding Modes: Investigating Protein Motifs That Regulate the Affinity of Isolated LG Domains 1-gen-2019 E Dempsey, Christopher; Giulia Bigotti, Maria; C Adams, Josephine; Brancaccio, Andrea
Molecular and structural basis of dystroglycanopathies 1-gen-2019 A. Cassetta; S. Covaceuszach; F. Sciandra; M. Bozzi; M. G. Bigotti; W. Hübner; A. Brancaccio
Synchrotron Radiation as a tool for the investigation of the structural basis of primary dystroglycanopathies. 1-gen-2019 Cassetta, Alberto; Covaceuszach, Sonia; Sciandra, Francesca; Bozzi, Manuela; Giulia Bigotti, Maria; Hübner, Wolfgang; Brancaccio, Andrea
A dystroglycan mutation (p.Cys667Phe) associated to muscle-eye-brain disease with multicystic leucodystrophy results in ER-retention of the mutant protein. 1-gen-2018 Signorino, Giulia; Covaceuszach, Sonia; Bozzi, Manuela; Hubner, Wolfgang; Monkemoller, Viola; Konarev Petr, V; Cassetta, Alberto; Brancaccio, Andrea; Sciandra, Francesca
Intraring allostery controls the function and assembly of a hetero-oligomeric class II chaperonin. 1-gen-2018 Shoemark, Dk; Sessions, Rb; Brancaccio, A; Bigotti, Mg
Live optical super-resolution microcospy applied to the characterization of maturation, localization and trafficking of defective dystroglycan mutants 1-gen-2018 Huber, W; Bozzi, M; Kerbs, A; Monkemoller, V; Sciandra, F; Bigotti, Mg; Brancaccio, A; Huser, T