PROVENZANO, CLAUDIA
PROVENZANO, CLAUDIA
Istituto di Biochimica e Biologia Cellulare - IBBC
Molecular Therapies for Myotonic Dystrophy Type 1: From Small Drugs to Gene Editing
2022 Izzo, Mariapaola; Battistini, Jonathan; Provenzano, Claudia; Martelli, Fabio; Cardinali, Beatrice; Falcone, Germana
Time-controlled and muscle-specific CRISPR/Cas9 mediated deletion of CTG-repeat expansion in the DMPK gene
2021 Cardinali, B; Provenzano, C; Izzo, M; Voellenkle, C; Battistini, J; Strimpakos, G; Golini, E; Mandillo, S; Scavizzi, F; Raspa, M; Perfetti, A; Baci, D; Lazarevic, D; Garciamanteiga, Jm; Gourdon, G; Martelli, F; Falcone, G
Design of novel small molecule base-pair recognizers of toxic CUG RNA transcripts characteristics of DM1
2020 Ondono, Raul; Lirio, Ángel; Elvira, Carlos; Álvarezmarimon, Elena; Provenzano, Claudia; Cardinali, Beatrice; Pérezalonso, Manuel; Perálvarezmarín, Alex; I Borrell, José; Falcone, Germana; Estradatejedor, Roger
High-throughput analysis of the RNAinduced silencing complex in myotonic dystrophy type 1 patients identifies the dysregulation of miR-29c and its target ASB2
2018 Cappella, Marisa; Perfetti, Alessandra; Cardinali, Beatrice; GarciaManteiga Jose, Manuel; Carrara, Matteo; Provenzano, Claudia; Fuschi, Paola; Cardani, Rosanna; Renna Laura, Valentina; Meola, Giovanni; Falcone, Germana; Martelli, Fabio
CRISPR/Cas9-MediatedDeletion ofCTGExpansions Recovers Normal Phenotype in Myogenic Cells Derived from Myotonic Dystrophy 1 Patients
2017 Provenzano, Claudia; Cappella, Marisa; Valaperta, Rea; Cardani, Rosanna; Meola, Giovanni; Martelli Beatrice Cardinali, Fabio; Falcone, Germana
MicroRNA-222 regulates muscle alternative splicing through Rbm24 during differentiation of skeletal muscle cells
2016 Cardinali B; Cappella M; Provenzano C; GarciaManteiga JM; Lazarevic D; Cittaro D; Martelli F; Falcone G.
MiR-21 is an Ngf-modulated MicroRNA That supports Ngf signaling and regulates neuronal degeneration in PC12 cells
2014 Montalban, E; Mattugini, N; Ciarapica, R; Provenzano, C; Savino, M; Scagnoli, F; Prosperini, G; Carissimi, C; Fulci, V; Matrone, C; Calissano, P; Nasi, S
Does the term 'trophic' actually mean anti-amyloidogenic? The case of NGF
2010 Calissano, P; Amadoro, G; Matrone, C; Ciafrè, S; Marolda, R; Corsetti, V; Ciotti, Mt; Mercanti, D; Di Luzio, A; Severini, C; Provenzano, C; Canu, N
Large scale analysis of transcription factor TTF-1/NKX2.1 target genes in GnRH secreting cell line GT1-7
2010 Provenzano, C; Pascucci, B; Lupari, E; Civitareale, D
Retinoblastoma protein acts as Pax 8 transcriptional coactivator.
2005 Miccadei S.; Provenzano C.; Mojzisek M.; Natali P.G.; Civitareale D..
v-Src inhibits myogenic differentiation by interfering with the regulatory network of muscle-specific transcriptional activators at multiple levels
2003 Falcone G.; Ciuffini L.; Gauzzi M.C.; Provenzano C.; Strano S.; Castellani L.;Alemà S
Glucocorticoids modulate transformation by v-Src in a cell-specific manner.
2002 Provenzano, C; Alemà, S; Falcone, G
A dominant-negative peroxisome proliferator-activated receptor gamma (PPAR gamma) mutant is a constitutive repressor and inhibits PPAR gamma-mediated adipogenesis
2000 Gurnell, M; Wentworth, JM; Agostini, M; Adams, M; Collingwood, TN; Provenzano, C; Browne, PO; Rajanayagam, O; Burris, TP; Schwabe, JW; Lazar, MA; Chatterjee, VKK
Eps8, a tyrosine kinase substrate, is recruited to the cell cortex and dynamic F-actin upon cytoskeleton remodeling.
1998 Provenzano C; Gallo R; Carbone R; Di Fiore PP; Falcone G; Castellani L; Alemà S
Regulation of the tyrosine kinase substrate Eps8 expression by growth factors, v-Src and terminal differentiation.
1997 Gallo, R; Provenzano, C; Carbone, R; Di Fiore, Pp; Castellani, L; Falcone, G; Alemà, S
Maintenance of the differentiated state in skeletal muscle: activation of v-Src disrupts sarcomeres in quail myotubes
1995 Castellani, L; Reedy, Mc; Gauzzi, Mc; Provenzano, C; Alemà, S; Falcone, G
Transformation of NIH3T3 cells by Rous sarcoma virus occurs with high efficiency in the absence of proviral rearrangements or amplification.
1992 Falcone G; Provenzano C; Alemà S; Tatò F
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Molecular Therapies for Myotonic Dystrophy Type 1: From Small Drugs to Gene Editing | 1-gen-2022 | Izzo, Mariapaola; Battistini, Jonathan; Provenzano, Claudia; Martelli, Fabio; Cardinali, Beatrice; Falcone, Germana | |
Time-controlled and muscle-specific CRISPR/Cas9 mediated deletion of CTG-repeat expansion in the DMPK gene | 1-gen-2021 | Cardinali, B; Provenzano, C; Izzo, M; Voellenkle, C; Battistini, J; Strimpakos, G; Golini, E; Mandillo, S; Scavizzi, F; Raspa, M; Perfetti, A; Baci, D; Lazarevic, D; Garciamanteiga, Jm; Gourdon, G; Martelli, F; Falcone, G | |
Design of novel small molecule base-pair recognizers of toxic CUG RNA transcripts characteristics of DM1 | 1-gen-2020 | Ondono, Raul; Lirio, Ángel; Elvira, Carlos; Álvarezmarimon, Elena; Provenzano, Claudia; Cardinali, Beatrice; Pérezalonso, Manuel; Perálvarezmarín, Alex; I Borrell, José; Falcone, Germana; Estradatejedor, Roger | |
High-throughput analysis of the RNAinduced silencing complex in myotonic dystrophy type 1 patients identifies the dysregulation of miR-29c and its target ASB2 | 1-gen-2018 | Cappella, Marisa; Perfetti, Alessandra; Cardinali, Beatrice; GarciaManteiga Jose, Manuel; Carrara, Matteo; Provenzano, Claudia; Fuschi, Paola; Cardani, Rosanna; Renna Laura, Valentina; Meola, Giovanni; Falcone, Germana; Martelli, Fabio | |
CRISPR/Cas9-MediatedDeletion ofCTGExpansions Recovers Normal Phenotype in Myogenic Cells Derived from Myotonic Dystrophy 1 Patients | 1-gen-2017 | Provenzano, Claudia; Cappella, Marisa; Valaperta, Rea; Cardani, Rosanna; Meola, Giovanni; Martelli Beatrice Cardinali, Fabio; Falcone, Germana | |
MicroRNA-222 regulates muscle alternative splicing through Rbm24 during differentiation of skeletal muscle cells | 1-gen-2016 | Cardinali B; Cappella M; Provenzano C; GarciaManteiga JM; Lazarevic D; Cittaro D; Martelli F; Falcone G. | |
MiR-21 is an Ngf-modulated MicroRNA That supports Ngf signaling and regulates neuronal degeneration in PC12 cells | 1-gen-2014 | Montalban, E; Mattugini, N; Ciarapica, R; Provenzano, C; Savino, M; Scagnoli, F; Prosperini, G; Carissimi, C; Fulci, V; Matrone, C; Calissano, P; Nasi, S | |
Does the term 'trophic' actually mean anti-amyloidogenic? The case of NGF | 1-gen-2010 | Calissano, P; Amadoro, G; Matrone, C; Ciafrè, S; Marolda, R; Corsetti, V; Ciotti, Mt; Mercanti, D; Di Luzio, A; Severini, C; Provenzano, C; Canu, N | |
Large scale analysis of transcription factor TTF-1/NKX2.1 target genes in GnRH secreting cell line GT1-7 | 1-gen-2010 | Provenzano, C; Pascucci, B; Lupari, E; Civitareale, D | |
Retinoblastoma protein acts as Pax 8 transcriptional coactivator. | 1-gen-2005 | Miccadei S.; Provenzano C.; Mojzisek M.; Natali P.G.; Civitareale D.. | |
v-Src inhibits myogenic differentiation by interfering with the regulatory network of muscle-specific transcriptional activators at multiple levels | 1-gen-2003 | Falcone G.; Ciuffini L.; Gauzzi M.C.; Provenzano C.; Strano S.; Castellani L.;Alemà S | |
Glucocorticoids modulate transformation by v-Src in a cell-specific manner. | 1-gen-2002 | Provenzano, C; Alemà, S; Falcone, G | |
A dominant-negative peroxisome proliferator-activated receptor gamma (PPAR gamma) mutant is a constitutive repressor and inhibits PPAR gamma-mediated adipogenesis | 1-gen-2000 | Gurnell, M; Wentworth, JM; Agostini, M; Adams, M; Collingwood, TN; Provenzano, C; Browne, PO; Rajanayagam, O; Burris, TP; Schwabe, JW; Lazar, MA; Chatterjee, VKK | |
Eps8, a tyrosine kinase substrate, is recruited to the cell cortex and dynamic F-actin upon cytoskeleton remodeling. | 1-gen-1998 | Provenzano C; Gallo R; Carbone R; Di Fiore PP; Falcone G; Castellani L; Alemà S | |
Regulation of the tyrosine kinase substrate Eps8 expression by growth factors, v-Src and terminal differentiation. | 1-gen-1997 | Gallo, R; Provenzano, C; Carbone, R; Di Fiore, Pp; Castellani, L; Falcone, G; Alemà, S | |
Maintenance of the differentiated state in skeletal muscle: activation of v-Src disrupts sarcomeres in quail myotubes | 1-gen-1995 | Castellani, L; Reedy, Mc; Gauzzi, Mc; Provenzano, C; Alemà, S; Falcone, G | |
Transformation of NIH3T3 cells by Rous sarcoma virus occurs with high efficiency in the absence of proviral rearrangements or amplification. | 1-gen-1992 | Falcone G; Provenzano C; Alemà S; Tatò F |